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Publications

This page provides research papers and publications that may help guide management for the medical professional with a patient with Vascular Ehlers-Danlos Syndrome (VEDS). Have a specific question about caring for someone with VEDS? Get connected with an expert.

Some of the features of VEDS are common in the general population; however, treatment is sometimes more complex because of the underlying connective tissue disorder. In addition, there are important considerations because the condition affects multiple body systems.

Diagnosis, natural history, and management in Vascular Ehlers–Danlos Syndrome

Byers, et al. 2017

https://onlinelibrary.wiley.com/doi/full/10.1002/ajmg.c.31553


A multi-institutional experience in Vascular Ehlers-Danlos Syndrome diagnosis

Shalhub, et al. 2019

https://www.ncbi.nlm.nih.gov/pubmed/31353273


Spontaneous pneumothorax and hemothorax frequently precede the arterial and intestinal complications of vascular Ehlers-Danlos syndrome.

Shalhub, Neptune, et al. 2019

https://www.ncbi.nlm.nih.gov/pubmed/30793832


A multi-institutional experience in the aortic and arterial pathology in individuals with genetically confirmed Vascular Ehlers-Danlos Syndrome.

Shalhub, Byers, et al. 2019

https://www.ncbi.nlm.nih.gov/pubmed/31126764


Molecular diagnosis in Vascular Ehlers-Danlos Syndrome predicts pattern of arterial involvement and outcomes.

Shalhub, Black, et al. 2014

https://www.ncbi.nlm.nih.gov/pubmed/24650746


Intestinal Perforation in Children as an Important Differential Diagnosis of Vascular Ehlers-Danlos Syndrome

Keon Young Park, et al. 2019

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6664867/


Bowel perforation in type IV Vascular Ehlers-Danlos Syndrome. A systematic review.

El-Masri, et al. 2018

https://www.ncbi.nlm.nih.gov/pubmed/29700641


Management of colonic complications of type IV Ehlers-Danlos Syndrome: a systematic review and evidence-based management strategy.

Speake, et al. 2019

https://www.ncbi.nlm.nih.gov/pubmed/31260161/


Audit of Gastrointestinal Manifestations in Patients with Loeys–Dietz Syndrome and Vascular Ehlers–Danlos Syndrome

Wang, et al. 2020

https://rdcu.be/b3Ei8


FDA Warning on the use of Fluoroquinolones

FDA Warning: Fluoroquinolones


Arterial Complications of vascular Ehlers-Danlos Syndrome

Eagleton, 2016

https://www.jvascsurg.org/article/S0741-5214(16)30876-X/fulltext


Safety of Endoscopy in Heritable Connective Tissue Disorders

Kilaru, et al. 2019

https://pubmed.ncbi.nlm.nih.gov/31185005/


Iliac Artery Pathology Presentation and Management in Vascular Ehlers-Danlos Syndrome

Shalhub, et al. 2022

https://doi.org/10.1016/j.jvs.2021.12.031


Surveillance and monitoring in vascular Ehlers-Danlos syndrome in European Reference Network for Rare Vascular Diseases (VASCERN)

Michael Frank, et al. 2022

https://doi.org/10.1016/j.ejmg.2022.104557


The role of cutaneous manifestations in the diagnosis of the Ehlers‐Danlos syndromes

Burrows, et al. 2022

https://doi.org/10.1002/ski2.140


Endovascular treatment of aortic aneurysms and dissections in patients with genetically triggered aortic diseases

Kolbel et al. 2022

https://doi.org/10.1053/j.semvascsurg.2022.06.001


Pain and fatigue in adults with Loeys–Dietz syndrome and vascular Ehlers–Danlos syndrome, a questionnaire‐based study

Heidi et al. 2022

https://doi.org/10.1002/ajmg.a.62858


Evaluating perinatal and neonatal outcomes among children with vascular Ehlers–Danlos syndrome

Morris et al. 2022

https://doi.org/10.1016/j.gim.2022.07.010


Operative repair of right intrathoracic subclavian artery aneurysms in patients with genetic arteriopathy

Shalhub et al. 2022

https://doi.org/10.1016/j.jvscit.2022.11.018


2022 ACC/AHA Guideline for the Diagnosis and Management of Aortic Disease: A Report of the American Heart Association/American College of Cardiology Joint Committee on Clinical Practice Guidelines

Isselbacher E, Preventza O, et al.

https://doi.org/10.1016/j.jacc.2022.08.004

If you need more information about the management of Vascular Ehlers-Danlos Syndrome for your patient, don’t hesitate to reach us through our Help and Resource Center.

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